High-protein foods to avoid
Preparing low-protein mealsa
It’s important to maintain a low-protein diet as part of your
Instead of this
treatment. Please consult with your doctor or dietitian to
help create a meal plan that works for you.
Meat with vegetables
Try this low-protein alternative
Instead of this
Vegetables
• With a low-protein sauce or dressing
Macaroni and cheese
Try this low-protein alternative
Low-protein macaroni and low-protein
cheese powder
Grated vegetables (zucchini, parsnip,
carrot, etc)
Meat (including beef, pork, and
lamb), chicken, and fish
Quiche
Preparing meals:
cooking the low-protein way
Substitute: roasted vegetables
• Baked with herbs
• With a low-protein pasta sauce
stirred through and a low-protein
bread crumb topping
Milk, cheese, and other dairy
Meal planning
Learning to cook
for someone on a
special diet takes
time. It might seem
challenging at first,
but it gets easier. Here
are some recipe ideas
to get you cooking the
low-protein way.
Grilled meat and
Substitute: rice milk, coconut milk, almond milk,
imitation or low-protein cheese
steamed vegetables
Stir-fry with rice or
noodles
Beans (including soy) and legumes
Low-protein spaghetti with meatless
Spaghetti Bolognese
tomato sauce; use low-protein
and salad
meatball alternative made from
vegetables, not soy
Fried or baked zucchini or eggplant
slices with bread crumb topping and
steamed vegetables
Adapted from the ASIEM Low Protein Handbook for Urea Cycle Disorders.
Stir-fry vegetables and low-protein rice
or pasta with an MSG-free sauce (eg,
sweet and sour sauce)
Grilled portabella mushroom or a
Substitute: low-protein rice or pasta
Hamburger
low-protein meat alternative patty
made from vegetables on low-protein
toasted bread or roll
Nuts and seeds
Low-protein bread (or pizza base made
Substitute: fruits such as apples, apricots,
blueberries, strawberries, or grapes
Pizza
with low-protein flour) spread with
tomato paste and topped with grilled
vegetables and low-protein cheese
Barbecue
a
Barbecued vegetable and fruit skewers
with low-protein bread or pasta salad
Low-protein does not always mean low-calorie.
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Calculating protein in your diet
Understanding how much protein you need is an
important part of managing your diet. To count grams of
protein, you will need to use information from food labels.
INDICATIONS AND USAGE
WHAT IS RAVICTI™ (glycerol phenylbutyrate) liquid?
RAVICTI is a prescription medicine used in adults and children 2 years of
age and older for long-term management of high blood levels of ammonia
(hyperammonemia) caused by a condition called a urea cycle disorder
(UCD). RAVICTI should be used if the UCD cannot be managed with a
low-protein diet and dietary supplements alone. RAVICTI must be used
along with a low-protein diet and, in some cases, dietary supplements.
The most common side effects of RAVICTI in children include:
• upper abdomen (stomach) pain
• nausea
• vomiting
• diarrhea
• decreased appetite
• high blood levels of ammonia
• headache
RAVICTI is not used for the treatment of hyperammonemia in people
with UCDs.
Tell your doctor if you have any side effect that bothers you or that does
not go away. These are not all of the possible side effects of RAVICTI. Call
your doctor for medical advice about side effects.
It is not known if RAVICTI is safe and effective for the treatment of
N-acetylglutamate synthase (NAGS) deficiency.
Calculating protein
in your diet
Making healthy
choices
People with urea
cycle disorders (UCDs)
cannot eliminate
ammonia, which is a
waste product from
digested protein.
UCDs are treated with
a special diet and
medications, and each
person’s treatment
plan is unique. Your
dietitian will advise
you on your specific
diet needs.
To calculate how
much protein you’re
getting:
It is not known if RAVICTI is safe and effective in children 2 months
to less than 2 years of age.
IMPORTANT SAFETY INFORMATION
Who Should Not Take RAVICTI:
• Children less than 2 months of age should not take RAVICTI
because it may not be digested in babies less than 2 months of age.
• Do not take RAVICTI if you are allergic to phenylbutyrate.
• RAVICTI is not used for the treatment of hyperammonemia in
people with UCDs.
• It is not known if RAVICTI is safe and effective for the treatment
of N-acetylglutamate synthase (NAGS) deficiency.
• It is not known if RAVICTI is safe and effective in children 2 months
to less than 2 years of age.
1)Start by checking
the serving size.
2)Check the amount
of protein.
3)Multiply the
amount of protein
by the amount of
servings.
In this example,
1 serving size =
1/4 c or 30 g, and there are
5 g of protein per serving
If you eat 2
servings (1/2 c):
2 servings x 5 g of protein =
10 g of protein
RAVICTI May Cause Serious Side Effects
Phenylacetate, a breakdown product of RAVICTI, may cause nervous
system side effects. Call your doctor or get medical help right away if
you get any of these symptoms while taking RAVICTI:
• sleepiness
• change in taste
• weakness
• problems with hearing
• lightheadedness
• confusion
• problems with memory
• headache
• worsening neuropathy (numbness,
tingling, or burning in your hands or feet)
What Are The Possible Side Effects Of RAVICTI?
The most common side effects of RAVICTI in adults include:
• diarrhea
• nausea
• decreased appetite
• gas
• vomiting
• high blood levels of ammonia
• headache
• tiredness • dizziness
Before You Take RAVICTI, Tell Your Doctor If You:
• Have liver or kidney problems
• Have pancreas or bowel (intestine) problems
• Have any other medical conditions
• Are pregnant or plan to become pregnant. It is not known if RAVICTI
will harm your unborn baby.
• Are breastfeeding or plan to breastfeed. It is not known if RAVICTI
passes into your breast milk. RAVICTI may harm your baby, so you
and your doctor should decide if you will take RAVICTI or breastfeed.
You are encouraged to report negative side effects of prescription
drugs to the FDA. Visit www.fda.gov/medwatch or call 1-800-FDA-1088.
You may also contact the Hyperion Therapeutics Medical Information
Department toll-free at 1-855-UCD-SUPT (1-855-823-7878) or
[email protected].
For more information about RAVICTI, please see the Medication Guide
attached to the full Prescribing Information in the patient brochure
enclosed in this kit.
RAVICTI is a trademark of Hyperion Therapeutics, Inc.
© 2013 Hyperion Therapeutics, Inc. All rights reserved.
P2013015.00 Printed in USA.
www.ravicti.com