AA Japan Long QT Syndrome Booklet.indd

長い質問商品
The Heart Rhythm Charity
Promoting better understanding, diagnosis,
treatment and quality of life for individuals
with cardiac arrhythmias
長い質問商品
www.heartrhythmcharity.org.uk
Registered Charity No. 1107496 ©2010
㧨⴫⚕㧪
QT ᑧ㐳∝୥⟲
ࠕ࡝ࠬࡒࠕ࡮ࠕ࡜ࠗࠕࡦࠬ
The Heart Rhythm Charity 㧔ᔃᜉ࠴ࡖ࡝࠹ࠖ࡯㧕
⑳ߚߜߪ‫ޔ‬ᔃਇᢛ⣂ߩࠃࠅ⦟޿ℂ⸃ߣ‫ޔ‬ㆡಾߥᴦ≮߿⸻ᢿߩଦㅴ‫ޔ‬ᖚ⠪ߐࠎߩ㧽㧻㧸㧔↢ᵴߩ⾰㧕ߩะ਄ࠍ߼
ߑߒߡ޿߹ߔ‫ޕ‬
㧨㧝ࡍ࡯ࠫ⋡એ㒠㧪
QT ᑧ㐳∝୥⟲ߦߟ޿ߡ
ߎߩౠሶߦߪ‫ޔ‬QT ᑧ㐳∝୥⟲ߦ㑐ߔࠆᖱႎ߇ឝタߐࠇߡ޿߹ߔ‫ࠆ޽ߦߎߎޕ‬ᖱႎߪ‫⺞ޔ‬ᩏ࡮⎇ⓥ߿ᖚ⠪ߐࠎ
ߩ⚻㛎߆ࠄᓧࠄࠇߚ߽ߩߢߔ‫ߊߒ⹦ߣߞ߽ޕ‬⍮ࠅߚ޿ᣇߪ‫ޔ‬ౠሶߢ⚫੺ߐࠇߡ޿ࠆ࠙ࠚࡉࠨࠗ࠻߽ߏⷩߊߛߐ޿‫ޕ‬
ࠕ࡝ࠬࡒࠕ࡮ࠕ࡜ࠗࠕࡦࠬ㧔A-A㧕ߪ‫ޔ‬୘ੱ‫ޔ‬ᖚ⠪ળ‫ޔ‬ᘏༀ࿅૕‫ޔ‬ක≮࿅૕ߣක≮⠪ࠣ࡞࡯ࡊߩㅪ៤߆ࠄߥࠆ
⚵❱ߢߔ‫ޕ‬
࿅૕ߪߘࠇߙࠇ⁛┙ߒߡ޿߹ߔ߇‫ޔߢߣ߽ߩࠬࡦࠕࠗ࡜ࠕ࡮ࠕࡒࠬ࡝ࠕޔ‬ㆡಾߢലᨐ⊛ߥ⸻ᢿߣᴦ≮ߩ᥉෸࡮
ଦㅴߩߚ߼ߦ‫ߦ߽ߣޔ‬ᵴേࠍⴕߞߡ޿߹ߔ‫ޕ‬
A-A ߪ‫ߩࠄࠇߎޔ‬࿅૕ߩ⋡ᮡߣ⋡⊛ࠍᡰᜬߒߡ޿߹ߔ‫ޕ‬
⋡ᰴ
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ߪߓ߼ߦ
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QT ᑧ㐳∝୥⟲ߣߪ㧫
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QT 㑆㓒ߣߪ㧫
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QT ᑧ㐳∝୥⟲ߩ∝⁁ߣߪ㧫
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QT ᑧ㐳∝୥⟲ߩේ࿃ߪ㧫
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QT ᑧ㐳∝୥⟲ߩෂ㒾ᕈߣߪ㧫
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ᬌᩏߣ⸻ᢿߦߟ޿ߡ
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∛ᱧߣ⹏ଔߦߟ޿ߡ
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ㆮવሶᬌᩏߦߟ޿ߡ
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ᴦ≮ᴺߦߟ޿ߡ
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↢ᵴࠬ࠲ࠗ࡞ߣᴦ≮ᓟߦߟ޿ߡ
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⼊๔
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ଢ೑ߥ࠙ࠚࡉࠨࠗ࠻
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߽ߞߣ⍮ࠅߚ޿ᣇ߳
↪⺆⸃⺑
ਇᢛ⣂
ᔃᜉߩ࡝࠭ࡓߩ㓚ኂ
ᔃ⤳⑼ක
ᔃ∔ᖚߩኾ㐷ኅ‫ޕ‬ᔃ∔ᖚߩ⸻ᢿ߿ᴦ≮ߦ޽ߚࠆ
ᔃ㔚࿑㧔ECG㧕
12 ᧄߩ࡝࡯࠼ߣ๭߫ࠇࠆࡢࠗࡗ࡯ࠍ↪޿ߡ‫ޔ‬ᔃ⤳ߩ㔚᳇⊛ᵴേࠍ⸥㍳ߔࠆⵝ⟎
ICD
ᬀ߃ㄟߺဳ㒰⚦േེ‫ޕ‬ᔃᜉࠍࡕ࠾࠲࡯ߔࠆ
ࡍ࡯ࠬࡔ࡯ࠞ࡯
⊹ਅߦᬀ߃ㄟ߹ࠇࠆዊߐߥ㊄ዻᕈߩᯏེߢ‫ޔ‬㔚᳇ೝỗࠍ⊒↢ߐߖߡਇᢛ⣂ࠍᴦ≮ߔࠆߩߦ↪޿ࠆ
ᄬ␹㧔syncope㧕
⣖߳ߩ㉄⚛ߩଏ⛎߇ᕆߦᱛ߹ࠆߎߣߦࠃߞߡ⿠ߎࠆ᳇⛘
QT ᑧ㐳∝୥⟲ߣߪ㧫
QT ᑧ㐳∝୥⟲ߣߪ‫ޔ‬ᔃ⤳ߩᯏ᪾⊛ᯏ⢻ߦ໧㗴߇ߥ޿ߩߦ߽߆߆ࠊࠄߕ‫ޔ‬㔚᳇ೝỗવ㆐ࠪࠬ࠹ࡓ߇㓚ኂߐࠇࠆ
∛᳇ߢߔ‫⚿ޕ‬ᨐߣߒߡ‫ߣޠࡦࡢࡐ࡮࠼࡯ࠨ࡞࠻ޟ‬๭߫ࠇࠆ㗫⣂ᕈਇᢛ⣂߇⿠ߎࠆߎߣ߇޽ࠅ߹ߔ‫ߩߎޕ‬ਇᢛ⣂߇
⿠ߎߞߚ႐ว‫ޔ‬ᔃ⤳߆ࠄⴊᶧ߇ᜉ಴ߐࠇߥߊߥࠅ‫ޔ‬⣖߇ή㉄⚛⁁ᘒߦߥࠅ‫ޔ‬ᄬ␹ߥߤࠍᒁ߈⿠ߎߒ߹ߔ‫ޕ‬⒘ߦߢ
ߔ߇‫⓭ޔ‬ὼᱫߩේ࿃ߦ߽ߥࠅ߹ߔ‫ޕ‬
QT ᑧ㐳∝୥⟲ߦࠃࠆਇᢛ⣂ߪ‫ޔ‬ㆇേ߿ࠬ࠻࡟ࠬߦࠃߞߡᒁ߈⿠ߎߐࠇࠆߎߣ߇޽ࠅ߹ߔ‫ޕ‬QT ᑧ㐳∝୥⟲ߦ
߆߆ߞߡ޿ࠆੱ߇⊝‫ޔ‬ਇᢛ⣂ࠍᒁ߈⿠ߎߔࠊߌߢߪ޽ࠅ߹ߖࠎ߇‫ߚߞߎ⿠ޔߒ߽ޔ‬㓙ߦߪ‫ޔ‬㕖Ᏹߦෂ㒾ߥ⁁ᘒߦ
ߥࠅ߹ߔ‫ޕ‬
QT 㑆㓒ߣߪ㧫
ᔃ⤳߇ᜉേߔࠆߩߪ‫ޔ‬㔚᳇ೝỗ߇ᔃ╭ో૕ߦᐢ߇ߞߡᔃ╭ࠍ෼❗ߐߖࠆߚ߼ߢߔ‫ޕ‬QT 㑆㓒ߪ‫ޔ‬ᔃ⤳ߩ㔚᳇ೝ
ỗᵴേࠍ⸥㍳ߔࠆ ECG㧔ᔃ㔚࿑㧕਄ߩ 12 ᧄߩ࡝࡯࠼਄ߢ⸘᷹ߐࠇ߹ߔ‫ޕ‬೨ᓟߒ߹ߒߚ߇‫ޔ‬QT 㑆㓒ߣߪ‫ޔ‬ᔃ⤳
߇㔚᳇ೝỗࠍ⊒ߒߡ߆ࠄ‫ޔ‬ᰴߩೝỗࠍ⊒ߔࠆḰ஻߇ߢ߈ࠆ߹ߢߩᤨ㑆ࠍᜰߒ߹ߔ‫ޕ‬QT 㑆㓒ߪ‫ޔ‬ᔃ㔚࿑਄ߦ߅ߌ
ࠆ․ቯߩ㧞ὐ㑆ߩ㑆㓒㧔QRS complex ߩ㐿ᆎὐ߆ࠄ T ᵄߩ⚳ᧃㇱ㧕ࠍᜰߒ‫⇣߇ࠇߘޔ‬Ᏹߦ㐳ߊߥࠆߎߣࠍ‫ޟ‬QT
㑆㓒ߩᑧ㐳‫ߣޠ‬๭߮߹ߔ‫ޕ‬
QT ᑧ㐳∝୥⟲ߩ∝⁁
QT ᑧ㐳∝୥⟲ߩᦨೋߩ∝⁁ߪ‫ޔ‬ᄙߊߩ႐ว‫ޔ‬ᐜዋᦼߦ⃻ࠇ߹ߔ‫ߪߡߒߣ⁁∝ޕ‬એਅߩࠃ߁ߥ߽ߩ߇޽ࠅ߹ߔ‫ޕ‬
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⓭ὼߩේ࿃ਇ᣿ߩᄬ␹㧔․ߦ‫ࠍࠬ࡟࠻ࠬޔ‬ᗵߓࠆ⁁ᴫߦ⟎߆ࠇߚ႐วߦ⃻ࠇࠆ㧕
‫࡯࡝࠹ࠬࡅޟޔߊࠃޕ‬෻ᔕ‫ޠ‬
ߣ⺋⸻ߐࠇࠆߎߣ߇޽ࠅ߹ߔ
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ේ࿃ਇ᣿ߩ∨ᡨ⊒૞‫⓭ޕ‬ὼߩᗧ⼂ᶖᄬߪ‫⊒ࠎ߆ࠎߡޔ‬૞ߣ⺋⸻ߐࠇࠆߎߣ߇޽ࠅ߹ߔ
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ᔃ⤳ߦ᭴ㅧ⊛ߥᰳ㒱߽‫ޔ‬㓚ኂ߽⷗ߟ߆ࠄߥ޿ߩߦ⿠ߎࠆ⓭ὼߩᔃ஗ᱛ߿⓭ὼᱫ‫⓭ޕ‬ὼߩᔃ஗ᱛ߿⓭ὼᱫߩ߅
ࠃߘ 10%ߪ‫ޔ‬QT ᑧ㐳∝୥⟲ߩೋ⊒∝⁁߇ේ࿃ߢߔ
QT ᑧ㐳∝୥⟲ߩේ࿃
QT ᑧ㐳∝୥⟲ߪ‫ޔ‬వᄤᕈߩ߽ߩ߽޽ࠇ߫‫ޔ‬ᓟᄤᕈߩ߽ߩ߽޽ࠅ߹ߔ‫ޕ‬
ᓟᄤᕈ QT ᑧ㐳∝୥⟲ߪ‫ߩ‛⮎ޔ޿ߡ޿ߚޔ‬ᛩਈ߇ේ࿃ߢߔ‫ޕ‬
వᄤᕈ QT ᑧ㐳∝୥⟲ߪ‫ࠆ޽ޔ‬ㆮવሶߩᄌ⇣ߦࠃࠆ߽ߩߢ‫ޔ‬ኅᣖ߆ࠄฃߌ⛮߇ࠇࠆ႐ว߽޽ࠅ߹ߔ‫ޕ‬వᄤᕈ
QT ᑧ㐳∝୥⟲ߩ⊒↢㗫ᐲߪ‫ޕࠎߖ߹޿ߡߞ߆ࠊߛ߹ޔ‬
వᄤᕈ QT ᑧ㐳∝୥⟲ߦߪߐ߹ߑ߹ߥ࠲ࠗࡊ߇޽ࠅ‫ޔ‬ᜂᒰߩᔃ⤳ኾ㐷ක߇޽ߥߚߩ࠲ࠗࡊࠍ⺑᣿ߒߡߊࠇ߹ߔ‫ޕ‬
߽ߞߣ߽৻⥸⊛ߥవᄤᕈ QT ᑧ㐳∝୥⟲ߦ‫ޔ‬LQTS(long-QT syndrome)1,2,3 ߩ㧟⒳߇޽ࠅ߹ߔ‫ޕ‬ㆮવሶ࠹ࠬ
࠻ࠍฃߌࠆߎߣߢ‫ޔ‬LQTS ߩ⒳㘃ࠍ․ቯߢ߈߹ߔ‫ޕ‬
LQTS ࠲ࠗࡊ 1 ෸߮ 2 ߩ႐ว‫ޔ‬ᔃ⤳ౝߩࠞ࡝࠙ࡓ࠴ࡖࡦࡀ࡞߇໧㗴ࠍᒁ߈⿠ߎߒ߹ߔ‫ޔߪߢࡊࠗ࠲ߩࠄࠇߎޕ‬
ㆇേ߿♖␹⊛ࠬ࠻࡟ࠬߦࠃߞߡਇᢛ⣂߇⿠ߎࠆߎߣ߇޽ࠅ߹ߔ‫ ࡊࠗ࠲ޕ‬3 ߢߪ‫߇࡞ࡀࡦࡖ࠴ࡓ࠙࡝࠻࠽ޔ‬ේ࿃ߣ
ߥࠅ‫߿ᤨ⌁⌧ޔ‬቟㕒ᤨߩㆃ޿ᜉേ߇ᔃਇᢛ⣂ࠍᒁ߈⿠ߎߔ႐ว߇޽ࠅ߹ߔ‫ޕ‬
QT ᑧ㐳∝୥⟲ߩෂ㒾ᕈ
QT ᑧ㐳∝୥⟲ߪ㕖Ᏹߦ⒘ߥ∛᳇ߢߔ‫ޕ‬ኾ㐷ኅߦࠃࠇ߫‫ޔ‬7000 ੱߦ㧝ੱ⒟ᐲߣߐࠇߡ޿߹ߔ߇‫޿ߥࠇߐ⷗⊒ޔ‬
႐ว߽ᄙ޿ߩߢ‫ߩߎޔ‬ᢙሼߪᧂ⏕ቯߢߔ‫ޕ‬
߽ߒኅᣖߩਛߦ‫ޔ‬ේ࿃ਇ᣿ߩᔃ⤳⊒૞ߢᱫ੢ߒߚࠅ‫ޔ‬ේ࿃ਇ᣿ߩᄬ␹⊒૞߿∨ᡨ⊒૞ࠍ⿠ߎߒߚߎߣ߇޽ࠆੱ
߇޿ࠆ႐วߦߪ‫ޔ‬QT ᑧ㐳∝୥⟲ߦߥࠆෂ㒾ᕈ߇޽ࠆ߆߽ߒࠇ߹ߖࠎ‫ޕ‬
߹ߚ‫ޔ‬QT 㑆㓒ࠍᑧ㐳ߐߖࠆࠃ߁ߥ⮎ࠍ᦯↪ߒߡ޿ࠆ႐วߦ߽ෂ㒾ᕈ߇޽ࠅ߹ߔ‫ޕ‬කᏧߦ⋧⺣ߒ‫⃻ޔ‬࿷᦯↪ߒ
ߡ޿ࠆ⮎ߦ QT ᑧ㐳∝୥⟲ࠍ⺃⊒ߔࠆෂ㒾ᕈ߇ߥ޿߆ࠍ⏕⹺ߒߡߊߛߐ޿‫ޕ‬
ᬌᩏߣ⸻ᢿ
ᔃ㔚࿑
ᔃ㔚࿑ߦࠃࠅ‫ޔ‬ᔃ⤳ߩ㔚᳇ᵴേߩ࠴ࠚ࠶ࠢ߇ߢ߈߹ߔ‫ޕ‬12 ᧄߩ࡝࡯࠼ࠍ⢷ㇱߣᚻ⿷ߦߟߌ‫ޔ‬ᔃ⤳ߩ㔚᳇ᵴേ
ࠍ⸥㍳ߒ߹ߔ‫ޔߡߞࠃߦࠇߎޕ‬QT ᑧ㐳∝୥⟲ߩน⢻ᕈࠍ␜ߔ‫ޔ‬QT 㑆㓒ߩᑧ㐳ࠍ⊒⷗ߢ߈ࠆ႐ว߇޽ࠅ߹ߔ‫ޕ‬
᥉ㅢ‫ޔ‬ᮮߦߥߞߚ⁁ᘒߢᔃ㔚࿑ࠍขࠅ߹ߔ߇‫ޔ‬QT ᑧ㐳∝୥⟲ߩᖚ⠪ߐࠎߢ߽‫ޔ‬ᔅߕ QT 㑆㓒ߩᑧ㐳߇⏕⹺ߢ߈
ࠆߣߪ㒢ࠄߥ޿ߩߢ‫ޔ‬૗ᐲ߆ᔃ㔚࿑ᬌᩏࠍ➅ࠅ㄰ߔ߆‫ޔ‬៤Ꮺဳߩᔃ⤳ࡕ࠾࠲࡯ࠍ૶ߞߡ⛮⛯⊛ߦᔃ⤳ߩᵴേࠍࡕ
࠾࠲࡯ߔࠆᔅⷐ߇޽ࠆ႐ว߽޽ࠅ߹ߔ‫ޕ‬
ੱߦࠃߞߡߪ‫ޔ‬ㆇേਛߩߺߦ QT 㑆㓒ߩᑧ㐳߇⃻ࠇࠆ႐ว߽޽ࠅ߹ߔ‫ߩߘޕ‬႐วߦߪ‫ߥࡦ࡯ࠪࡑࠣࡦ࠾ࡦ࡜ޔ‬
ߤߢㆇേࠍߒߥ߇ࠄ‫ޔ‬ᔃ㔚࿑ᬌᩏࠍⴕ߁ᔅⷐ߇޽ࠅ߹ߔ‫ޕ‬
∛ᱧߣ⹏ଔ
ᔃ⤳ኾ㐷ක߆ࠄߪ‫߿⁁∝ޔ‬ኅᣖߩ∛ᱧߦߟ޿ߡߐ߹ߑ߹ߥ⾰໧ࠍฃߌ߹ߔ‫⃻ޕ‬࿷‫ߩ⮎ࠆ޿ߡߒ↪᦯ޔ‬⒳㘃߽ᔅ
ⷐߥᖱႎߢߔ‫ޔߚ߹ޕ‬ਇᢛ⣂ߩෂ㒾ᕈ߇਄߇ࠆ‫ⴊߪ޿ࠆ޽ޔ‬ᶧਛߩࠞ࡝࠙ࡓ࡟ࡌ࡞ࠍਅߍࠆࠃ߁ߥ⁁ᴫ㧔ㆊ೾ߥ
ཌྷฯ‫ޔ‬ਅ∯‫⚻␹ޔ‬ᕈή㘩᰼‫⁁↲ߪߚ߹ޔ‬⣼∔ᖚ㧕߇ߥ޿߆߽⡞߆ࠇࠆߢߒࠂ߁‫ⴊޕ‬ਛߩࠞ࡝࠙ࡓỚᐲࠍ⺞ߴࠆߚ
߼ߦⴊᶧᬌᩏ߇ⴕࠊࠇࠆߎߣ߽޽ࠅ߹ߔ‫ޕ‬
ㆮવሶᬌᩏ
߽ߒ‫ޔ‬ᜂᒰߩකᏧ߇ QT ᑧ㐳∝୥⟲ߩน⢻ᕈ߇޽ࠆߣ⸻ᢿߒߚ႐ว‫ޔ‬ㆮવሶᬌᩏߩኾ㐷ኅࠍ⚫੺ߐࠇࠆߎߣ߇
޽ࠅ߹ߔ‫ޕ‬ㆮવሶᬌᩏߩኾ㐷ኅߪ‫⥄ߚߥ޽ޔ‬り߿޽ߥߚߩኅᣖߦኻߒߡᬌᩏࠍⴕ޿‫ޔ‬QT ᑧ㐳∝୥⟲߆ߤ߁߆ࠍ
⸻ᢿߒ߹ߔ‫ޕ‬QT ᑧ㐳∝୥⟲ߪ‫ޔ‬႐วߦࠃߞߡߪ‫ޔ‬ᬌᩏߢ․ቯߢ߈ߥ޿ߎߣ߽޽ࠅ‫ޔ‬ᬌᩏ⚿ᨐ߇㒶ᕈߛߞߚߣߒ
ߡ߽‫ޔ‬QT ᑧ㐳∝୥⟲ߩน⢻ᕈ߇ߥ޿ߣߪ⸒޿ಾࠇ߹ߖࠎ‫ޕ‬
ᴦ≮ᴺ
ߐ߹ߑ߹ߥᴦ≮ᴺ߇޽ࠅ߹ߔߩߢ‫ޔ‬කᏧߣࠃߊ⋧⺣ߔࠆࠃ߁ߦߒߡߊߛߐ޿‫ޕ‬QT ᑧ㐳∝୥⟲ࠍቢోߦᴦߔᣇ
ᴺߪ޽ࠅ߹ߖࠎߩߢ‫ޔ‬ᴦ≮ߩਥ⋡⊛ߪ‫ޔ‬ᗧ⼂ᶖᄬ߿๮ߩෂ㒾ᕈ߇޽ࠆਇᢛ⣂ߩ㒐ᱛߦߥࠅ߹ߔ‫ޕ‬ᴦ≮ᴺߪ‫ޔ‬QT
ᑧ㐳∝୥⟲ߩ⒳㘃߿޽ߥߚߩ␠ળ⊛⢛᥊࡮⁁ᴫߦࠃߞߡ⇣ߥࠅ߹ߔ‫ޕ‬ਇᢛ⣂ߩ੍㒐ߦߪ‫ߊࠃޔ‬᛫ਇᢛ⣂⮎߇↪޿
ࠄࠇ߹ߔ‫ޕ‬QT ᑧ㐳∝୥⟲ߩ⒳㘃ߦࠃߞߡߪ‫ޔ‬ᔃᜉ߇㕖Ᏹߦㆃߊߥࠆߎߣ߇ਇᢛ⣂ߩᒁ߈㊄ߣߥࠆ႐ว߽޽ࠆߩ
ߢ‫ޔߡߞ૶ࠍ࡯ࠞ࡯ࡔࠬ࡯ࡍޔ‬ᔃᜉ߇ㆃߊߥࠄߥ޿ࠃ߁ߦߔࠆߎߣ߇޽ࠅ߹ߔ‫ޔߚ߹ޕ‬๮ߩෂ㒾ߦ߆߆ࠊࠆࠃ߁
ߥਇᢛ⣂ࠍᬌ⍮ߒߡ⥄േ⊛ߦ㔚᳇ᴦ≮ࠍᣉߔ ICD㧔ᬀ߃ㄟߺဳ㒰⚦േེ㧕ࠍ↪޿ࠆߣ޿ߞߚㆬᛯ⢇߽޽ࠅ߹ߔ‫ޕ‬
QT ᑧ㐳∝୥⟲ߩ⒳㘃ߦࠃߞߡߪ‫⑌ࠍ↪૶ߩ⸘ᤨߒ߹ⷡ⋡ޔ‬ᱛߐࠇߚࠅ‫ޔ‬ዞኢਛߦ៤Ꮺ㔚⹤߇㡆ࠄߥ޿ࠃ߁‫ޔ‬
㔚Ḯࠍಾߞߡ߅ߊࠃ߁ߦᜰ␜ߐࠇࠆߎߣ߽޽ࠅ߹ߔ‫ޕ‬
ㆇേߦࠃߞߡᄬ␹߇ᒁ߈⿠ߎߐࠇࠆ႐วߦߪ‫ޔ‬ỗߒ޿ㆇേߪㆱߌ߹ߒࠂ߁‫⼾߇ࡓ࠙࡝ࠞޔߚ߹ޕ‬ንߥ㘩ຠࠍ㘩
ߴࠆࠃ߁ߦߒ‫ࠍ࡞ࡌ࡟ࡓ࠙࡝ࠞޔ‬ਅߍߥ޿ࠃ߁ߦකᏧߦ㘩੐ߦ㑐ߒߡࠃߊ⋧⺣ߒ߹ߒࠂ߁‫ޕ‬
QT ᑧ㐳∝୥⟲ࠍᖚߞߡ޿ࠆߎߣࠍ๟࿐ߩੱߦવ߃‫ޔ‬ᄬ␹ߒߚ㓙ߦߪ‫ߦߋߔޔ‬ᢇᕆゞࠍ๭ࠎߢ߽ࠄ߃ࠆࠃ߁߅
㗿޿ߒߡ߅ߊߣ⦟޿ߢߒࠂ߁‫࡯ࠖ࠹࡝ࡖ࠴ޕ‬ᵴേߩਛߦߪ‫ޔ‬ᖚ⠪ᖱႎࠍ៤Ꮺߢ߈ࠆ ID ࡉ࡟ࠬ࡟࠶࠻ࠍ㈩Ꮣߒߡ
޿ࠆ߽ߩ߽޽ࠅ߹ߔ‫⼔⋴ޕ‬Ꮷ߿ਇᢛ⣂ߩኾ㐷ක߇‫ߦࠄࠇߎޔ‬㑐ߔࠆᖱႎࠍឭଏߒߡߊࠇ߹ߔ‫ޕ‬
QT ᑧ㐳∝୥⟲ߩᖚ⠪ߐࠎߩᔃᜉ࡝࠭ࡓߦᓇ㗀ࠍਈ߃ࠆ⮎ߪߚߊߐࠎ޽ࠅ߹ߔ‫⮎ޕ‬ዪߢ⾈߃ࠆߖ߈ᱛ߼߿㘑㇎
⮎‫ޔ‬᛫↢‛⾰‫ޔ‬᛫㝠೷߿‫ޔ‬᛫⌀⩶⮎‫ޔ‬ਇᢛ⣂ߩᴦ≮⮎ߥߤ߇ QT 㑆㓒ߦᓇ㗀ࠍਈ߃߹ߔ‫∛ޕ‬㒮ߢ૗߆⮎ࠍಣᣇߐ
ࠇߚࠄ‫ޔ‬ᔅߕකᏧ߿⮎೷Ꮷߦ⋧⺣ߒ‫ޔ‬QT ᑧ㐳∝୥⟲ߩᖚ⠪߇㘶ࠎߢ߽ᄢਂᄦ߆ࠍ⏕߆߼߹ߒࠂ߁‫ޕ‬QT ᑧ㐳∝
୥⟲ߦᓇ㗀ߔࠆ⮎ߦ㑐ߒߡߪ‫࠻ࠗࠨߩࠄߜߎޔ‬㧔http://www.qtdrugs.org㧕߆ࠄ⏕⹺ߢ߈߹ߔ‫ࡉࠚ࠙ޔߒ߆ߒޕ‬
ࠨࠗ࠻ߦឝタߐࠇߡ޿ߥ޿ᣂ⮎߽޽ࠅ߹ߔߩߢ‫ࠍ⮎ޔ‬ಣᣇߒߡ߽ࠄ߁㓙ߦߪᔅߕ‫ޔ‬QT ᑧ㐳∝୥⟲ߦ⟕ߞߡ޿ࠆ
ߎߣࠍ↳ߒ಴߹ߒࠂ߁‫ޕ‬
↢ᵴࠬ࠲ࠗ࡞ߣᴦ≮ᓟߦߟ޿ߡ
QT ᑧ㐳∝୥⟲ߩ⒳㘃ߦࠃߞߡߪ‫৻ޔ‬ቯߩㆇേ೙㒢ࠍฃߌࠆ႐ว߇޽ࠅ߹ߔ‫ޕ‬ㆇേ೙㒢ߩ࡟ࡌ࡞ߪ୘‫⇣ߢੱޘ‬
ߥࠅ߹ߔߩߢ‫ޔ‬කᏧ߿⋴⼔Ꮷߦ୘೎ߦ⋧⺣ߒ߹ߒࠂ߁‫⼊߿࠷࡯ࡐࠬޔߦࠄߐޕ‬ኤ㑐ଥ‫ޔ‬ᶖ㒐㑐ଥߩ઀੐ߦዞߎ߁
ߣߔࠆ႐วߦߪ৻ቯߩ೙㒢ࠍฃߌࠆߎߣ߇޽ࠅ߹ߔ‫ޕ‬⡯ᬺㆬᛯߦߟ޿ߡ߽කᏧߦ⋧⺣ߒ߹ߒࠂ߁‫ޕ‬
⼊๔
‫ߩߤߥޠࡦࠗࠞࠦޟ߿ޠ࡯ࠪ࠲ࠬࠢࠛޟ‬ᇅᭉ⊛ߥ㤗⮎ߪ QT ᑧ㐳∝୥⟲ߩᖚ⠪ߦߪ․ߦෂ㒾ߢ‫⥌ޔ‬๮⊛ߦߥࠆ
႐ว߽޽ࠅ߹ߔ‫߇⁁∝ޕ‬シ޿ᣇߢ߽‫ߚߒ߁ߎޔ‬㤗⮎ߪ⛘ኻߦ૶ࠊߥ޿ࠃ߁ߦߒ߹ߒࠂ߁‫ޕ‬
ଢ೑ߥ࠙ࠚࡉࠨࠗ࠻
ࠕ࡝ࠬࡒࠕ࡮ࠕ࡜ࠗࠕࡦࠬ UK ߩࠨࠗ࠻߆ࠄ‫ޔ‬ଢ೑ߥ࠙ࠚࡉࠨࠗ࠻ߩ࡝ࠬ࠻ࠍ⷗ߟߌࠄࠇ߹ߔ‫ߪ࠻ࠬ࡝ߩߎޕ‬
ᓢ‫ᦝߦޘ‬ᣂߐࠇߡ޿߹ߔ‫ߦ࠻ࠬ࡝ޔߒ߽ޕ‬タߞߡ޿ߥ޿࠙ࠚࡉࠨࠗ࠻߇޽ࠅ߹ߒߚࠄ‫ࡦࠕࠗ࡜ࠕ࡮ࠕࡒࠬ࡝ࠕޔ‬
ࠬ UK ߹ߢߏㅪ⛊ߊߛߐ޿߹ߔࠃ߁‫߅ޔ‬㗿޿↳ߒ޽ߍ߹ߔ‫ޕ‬
㔚⹤⇟ภ㧦+44 (0)1789-450-787‫ޔ‬email㧦[email protected]
૗߆⇼໧ὐ߿ਇ቟ߥὐ߇޽ࠇ߫‫ޔ‬කᏧ߿ᔃ⤳↢ℂ჻ߥߤߦ⋧⺣ߔࠆࠃ߁ߦߒ߹ߒࠂ߁‫ޕ‬
߽ߞߣ⍮ࠅߚ޿ᣇߪ̖̖
એਅߦ‫ࠬࡦࠕࠗ࡜ࠕ࡮ࠕࡒࠬ࡝ࠕޔ‬ᖚ⠪ࡉ࠶ࠢ࡟࠶࠻ߩ৻ⷩࠍឝタ޿ߚߒ߹ߔ‫ޕ‬
࡝ࠬ࠻
Executive Committee
President
Prof A John Camm
Mr Pierre Chauvineau
Dr Mathew Fay
Dr Gerry Kaye
Dr Francis Murgatroyd
Dr Derek Connelly
Dr Adam Fitzpatrick
Dr Nick Linker
Dr Kim Rajappan
Dr Campbell Cowan
Dr Michael Gammage
Mrs Trudie Lobban
Dr Richard Schilling
Dr Wyn Davies
Mrs Angela Griffiths
Ms Nicola Meldrum
Dr Graham Stuart
Dr Sabine Ernst
Dr Guy Haywood
Prof John Morgan
Mrs Jenny Tagney
Mr Nigel Farrell
Mrs Sue Jones
Mrs Jayne Mudd
Mr Paul Turner
Dr Derek Connelly
W B Beaumont, OBE
Mr Nigel Farrell
Trustees
Dr Adam Fitzpatrick
Patrons
Rt. Hon Tony Blair
Prof Silvia G Priori
endorsed by
Arrhythmia Alliance
PO Box 3697 Stratford upon Avon
Warwickshire CV37 8YL
Tel: +44 (0) 1789 450 787
e-mail: [email protected]
www.heartrhythmcharity.org.uk
Please remember these are general guidelines and individuals
should always discuss their condition with their own doctor.
Published 2008 revised April 2010
Mrs Trudie Lobban
Prof Hein J J Wellens